ABOUT PH
What is PH?
Pulmonary hypertension—or PH—is a condition characterized by high blood pressure in the pulmonary arteries (blood vessels) that carry blood to the lungs. Find out more on this page.
Do you ever wonder how to explain pulmonary hypertension? Are you new to PH? Watch and share our video explaining PH and spread PH awareness of your life in purple. Watch all videos here >
PH is often due to the narrowing and closing of some pulmonary arteries due to several abnormalities:
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vasoconstriction (narrowing of pulmonary arteries due to spasm)
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multiplication and growth of cells in the walls of pulmonary arteries
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microscopic (very small) blood clots in the pulmonary arteries
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scar tissue formation in the pulmonary arteries
The average (mean) pressure within the pulmonary arteries (also known as mPAP) is normally 10-20 mmHg. PH is diagnosed when mPAP is higher than 20 mmHg.
PH will often put a strain on the right side of the heart, specifically the right ventricle (RV). If left untreated, PH can lead to RV failure, a serious type of heart failure.
It is vitally important that those who are at-risk of having PH or newly diagnosed get referred to a PH specialist for the best possible care and treatment.
What is pulmonary hypertension (PH)?
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Persistent or unexplained shortness of breath (especially upon exertion)
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Fatigue/loss of energy
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Swollen ankles and legs (also called edema)
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Chest pain
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Bluish lips, hands, and feet
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Dizziness upon activity, including walking, climbing stairs
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Fainting (also called syncope)
What are the symptoms of PH?
The treatment of PH is focused on lowering the pulmonary artery pressure (PAP = blood pressure in the blood vessels that carry blood to the lungs), and improving the RV-type of heart failure. PH-physicians prescribe the available medications alone or in combination to help alleviate the symptoms and slow the progression of PH and RV failure. Once a combination of treatments is no longer effective, lung transplantation may be considered.
You can find an overview of available treatments in Canada by visiting this page.
PHA Canada is committed to ensuring fair and equitable access to PH medications for all Canadians. To find out more about our work advocating on behalf of the PH community, visit our Advocacy page.
How is PH treated?
Quick Facts
Many people with PH in Canada spend two to three years seeking an accurate diagnosis. Alarmingly, without treatment, the average life expectancy of a person with PH is less than three years.
No cure currently exists for PH, with the exception of CTEPH, which may be cured through surgery.
A number of treatments are approved in Canada to slow progression of PH and alleviate symptoms.
Centres specialized in the treatment of PH in adults and children are located throughout the country.
It is estimated that approximately 5,000 Canadians have been diagnosed with pulmonary hypertension, but as many as 10,000 may be affected by the condition.
PH can strike anyone regardless of age, sex, or social/ethnic background.
PH is often an invisible illness; people who have PH may not look sick, even though they are.
PH has significant financial, social, and emotional impacts on patients and their families.